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However, the general and mental condition was relatively better.
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The patient was discharged from the hospital.
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A 57 year old lady presented to a peripheral hospital with complaints of penetrating epigastric pain of a week’s duration.
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There was no vomiting or weight loss.
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Bowel movements were normal.
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Clinical examination at the time was unrevealing.
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An abdominal ultrasound examination was reported as normal.
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The patient’s insistence on full investigation of the persistent epigastric pain led to a computed tomographic examination and discovery of a pancreatic tumour subsequent to which she was referred to our institution.
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The CT scan showed a large tumour (6cm in largest diameter) in the body and tail of pancreas with no evidence of metastasis.
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She was prepared for exploratory laparotomy.
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The pancreas was explored through the gastrocolic omentum.
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The body and tail of the pancreas including the tumour were resected.
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The spleen was also removed.
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The end of the pancreas was suture ligated.
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Her post-operative recovery was uneventful.
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Histological examination of the specimen showed a well circumscribed ovoid tumour 60mm x 50mm across.
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Sections revealed islands and trabeculae of regular cells with variable amounts of eosinophilic cytoplasm, mostly regular nuclei with indistinct nucleoli.
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Areas of necrosis were present with hemorrhage.
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A fibrous pseudo-capsule was noted around the tumour and the resection of the tumour appeared complete.
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No capsular of vascular invasion was seen.
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Immuno-peroxidase staining was positive for chromogranin A.
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Synaptophysin was strongly positive, CD10 was negative, Ki-67 was less than 2% positive and the mitotic count was between 2-20 per 10 hpf.
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The staining reactions were confirmatory of a neuroendocrine carcinoma of the pancreas.
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The final staging of the completely excised tumour was T3 N0 M0.
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Following discharge, she was followed up regularly and remains symptom free.
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A CT Scan performed 2 years after surgery showed no evidence of tumour recurrence.
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A 3-day-old boy from Kosovo with dextro-transposition of the great arteries who developed progressive heart failure required an emergency arterial switch operation.
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Because of persistent pulmonary edema after completion of the arterial switch operation at our institution, the patient could not be weaned off mechanical ventilation.
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Transthoracic echocardiography revealed an anomalous accelerated flow, indicating an anomalous systemic pulmonary shunt.
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Arterial catheterization revealed an abnormal bronchial artery originating from the left subclavian artery and bifurcating to both lungs.
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The anomalous ectatic bronchial artery was successfully occluded by coil embolization.
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The improvement of the patient's hemodynamic status resulted in an uneventful post-operative course.
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A 49-year-old white Caucasian woman presented with vaginal bleeding.
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A pelvic examination revealed a cystic lesion arising from her cervix.
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Examination of a biopsy specimen revealed a poorly differentiated neoplasm, with sheets of small hyperchromatic cells, staining weakly for neuroendocrine markers.
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She was diagnosed with small cell carcinoma and started on concurrent chemotherapy and radiation.
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However, additional positive immunostaining for CD99 was strongly suggestive of Ewing's sarcoma.
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Fluorescence in situ hybridization revealed ESWR1 gene rearrangement, confirming Ewing's sarcoma.
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Our patient underwent surgery, which confirmed stage IIB Ewing's sarcoma.
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She received adjuvant chemotherapy but died from progressive metastatic disease after four cycles.
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This case report describes the condition of a 30-year-old man involved in a motor vehicle collision.
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Clinical examination, X-rays, and computed tomography scan revealed a posterior hip dislocation with an ipsilateral femoral head and mid-shaft fractures.
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The patient was treated by closed reduction of hip dislocation using a temporarily applied external fixator followed by intramedullary nailing of the femoral shaft.
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Achieving a closed reduction is a challenge with ipsilateral fractures but it should be favored over open reduction due to a lower risk of complications.
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The type of femoral head fracture, in this case, may have aided in an easier reduction.
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We present here a case of Macrophage activation syndrome associated with Griscelli syndrome type 2 in a 3-years-old male born of consanguineous parentage.
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His birth histories, his familie social history and developmental milestones were unremarkable.
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He was born at full term with no antenatal or perinatal complications, He was on exclusively breast-fed, food diversification was started at 6 months old, his weight, length and psychomotor development were within the normal range, the child was described as a good eater, was on a normal diet and was thriving appropriately.
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Furthermore the boy presented a progressive abdominal distension since birth, progressive pallor and recurrent episodes of fever since 1 year of age.
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There was history of blood transfusions for last 2 months.
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On the other side there was no history of jaundice, vomiting, urinary or bowel complaints, bleeding from any site or neurological complaints.
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On admission, he was very pale with silvery gray scalp hair, white eyelashes, he was hypotonic, tachycardic, fever of 40°C, lymphoadenopathy and hepato-splenomegaly.
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The blood count showed pancytopenia; 1980 white blood cells/µL (VN 4000-13 500/µL), neutrophils 820/µL, 910 cells/µL, hemoglobin (Hb) 6.3 g/dL (11.5-14 VN, 5 g/dL), platelets 44 000/µL (VN 150 000-400 000/µL), There were no giant cytoplasmic granules in leucocytes.
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The liver function tests were normal expect low albumin (2.1 mg/dL) and increased alkaline phosphatase (1196 mg/dL) with low fibrinogen (1.7g/l).
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Serum triglycerides, ferrintin and lactic dehydrogenase were very high; respectively 4.75g/L; 2763µg/L and 597U/L. the C reactive protein (CRP) was elevated at 83mg/l.
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A chest X-ray was normal while the abdominal ultrasound showed a hepatomegaly and a splenomegaly, free biliary ducts without ascites.
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Because of hepato-splenomegaly, pancytopenia, hyperferritinemia and hypofibrinogenemia the diagnosis of Macrophage activation syndrome was evoked indicating a bone marrow aspiration that showed numerous morphologically benign macrophages with haemophagocytic activity that comforting the diagnosis of a SAM according to Ravelli and HLH-2004 criteria.
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Blood culture, urine examination, malarial serology, Kala Azar serology, viral serologies such as EBV, hepatitis A, B, C and human immunodeficiency virus HIV, serologies of rickettsia, syphilis and toxoplasmosa were negatives.
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Serologies of CMV and rubella showed an old immunization.
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The immunological tests such as antinuclear antibodies (ANA), anti-LKM1, anti-mitochondria and anti-smooth muscle antibodies were negatives.
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Because of the consanguineous family, notion of recurrent infection and the presence of silvery-gray color of the hair and eyebrows, diagnosis of Griscelli Syndrome was evoked directing a light microscopy examination of the hair that showed a large, irregular clumps of pigments characteristic of Griscelli Syndrome.
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The molecular biology showed mutation in RAB27A gene confirming the diagnosis of a Griscelli syndrome type 2.
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The first-line therapy in management of Macrophage activation syndrome complicating Griscelli syndrome type 2 was based on the parenteral administration of high doses of corticosteroids (methylprednisolone pulses 1g/0.73m 2 /day for 3 days then 60mg/m 2) with poor response; persisting with involvement of the 3 cell lines in the blood count, elevated ferritin and triglycerides.
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Given the lack of response to steroids, Etoposide was started for 3 days associated with cyclophosphamide, the evolution was good with improvement of count blood cells, ferritin was lessening while the bone marrow showed decreased numerous of macrophages with low haemophagocytic activity.
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On the other side the infectious process was good managed by perfusion of Antibiotics such as Ceftazidim in combination with aminoside.
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The patient was sent home with prednisone and cyclosporine, He was placed on the list of bone marrow transplantation (BMT).
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A 23-year-old previously healthy man, presented to the hospital's emergency department, with a 3-day history of high-grade fever up to 40°C and upper right abdominal pain.
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The patient's past medical history was non-significant.
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He was a student and had not received any medication.
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He had a pet dog and reported no recent travel.
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During physical examination on admission, vital signs were normal and he was febrile with a body temperature of 38°C.
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Abdominal examination revealed a tender palpable liver, with no signs of peritoneal irritation.
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The remainder of physical examination was unremarkable.
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Abnormal laboratory results on admission included a white blood cell count (WBC) of 20.830 (4-10.5x10³/μL), elevated C-reactive protein (CRP) level (28mg/dl, normal ≤0.5mg/dl), slightly elevated alanine aminotransferase (ALT) of 56 IU/L (normal 5-40 IU/L), and lactic dehydrogenase (LDH) of 255 IU/L (normal <225 IU/L).
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Alkaline phosphatase (ALP) was normal.
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Abdominal ultrasonography on admission revealed a mildly enlarged liver and spleen and the presence of 2 sizable, hypoechoic lesions.
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Abdominal computed tomography (CT) scan revealed the 2 aforementioned lesions in diameter of 5.6cm at the left liver lobe and 5.2cm in the right lobe.
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The lesions were hypodense and presented peripheral enhancement after intravenous contrast, similar to the morphology of hepatic abscesses.
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The patient was admitted for further evaluation and treatment.
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Culture guided antimicrobials and appropriate drainage was our first option.
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Empiric antibiotic therapy with intravenous ciprofloxacin (400mg every 12 hours), and metronidazole (500mg every 8 hours) was initiated.
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All cultures resulted negative.
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Initially, we performed percutaneous sonographic (U/S) guided aspiration into the left hepatic abscess cavity.
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A thick, purulent material of 40cc was drained and sent for culture.
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Microbiology revealed a Gram-negative bacterium that presented slow growth.
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On the 5th and 8th days of admission, we performed CT guided catheter drainage of both abscesses.
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Meanwhile irregular spikes of fever with daytime variation accompanied by night sweats persisted.
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Ciprofloxacin discontinued and meropenem at a dose of 1gr every 8 hours administered.
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[ 1, 1, 0, 0, 0, 0, 0, 0, 0, 0, 0, 0, 1, 0 ]
Thorough screening for other possible sources of infection, resulted negative.
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[ 0, 1, 0, 0, 0, 0, 0, 0, 0, 0, 5, 0 ]
Transthoracic echocardiography was negative for vegetations and showed mild mitral regurgitation.
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[ "CUI_LESS", "CUI_LESS", "CUI_LESS", "CUI_LESS", "CUI_LESS", "C1285498", "CUI_LESS", "CUI_LESS", "C3551535", "C3551535", "C3551535", "CUI_LESS" ]
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Entamoeba histolytica Abs, echinococcus Abs, leismania Abs, brucella Abs were negative.
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Gastrointestinal endoscopic evaluation was unrevealing.
[ "Gastrointestinal", "endoscopic", "evaluation", "was", "unrevealing", "." ]
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[ 0, 0, 0, 0, 0, 0 ]
[ "CUI_LESS", "CUI_LESS", "CUI_LESS", "CUI_LESS", "CUI_LESS", "CUI_LESS" ]
[ 0, 0, 1, 0, 5, 0 ]
The patient was also HIV negative and no other immunodeficiency conditions were identified.
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[ 2, 7, 0, 0, 0, 1, 0, 0, 0, 0, 1, 0, 1, 0 ]
Eventually, the isolate identified by the Vitek 2 automated system and classified as A. aphrophilus.
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To confirm the identification of the strain we performed matrix assisted laser desorption ionization-time of flight mass spectrometry (MALDI-TOF MS).
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The sensitivity test was performed with minimal inhibitory concentration (MIC) test strips; the isolate's susceptibility was to ceftriaxone ≤0.125 (S), cefepime ≤0.5 (S), ciprofloxacin ≤0.125 (S), gentamycin ≤0.5 (S), amikacin ≤0.125 (S) and to meropenem ≤0.032 (S).
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Percutaneous drainage of both abscesses, combined with antimicrobial treatment, was successful and the patient's clinical condition improved.
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Thankfully, no surgical procedure was required.
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The drains were removed immediately the fluid from the abscess cavities became clear.
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Meropenem was administered for a total of 2 weeks.
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